Epithelioid sarcoma (ES) is a high-grade, soft tissue tumor of mesenchymal origin
that rarely occurs in children and is often misdiagnosed as a benign entity. We present
the case of a 12-year-old girl with a delayed diagnosis of ES of the left thumb. Radiological
examination showed possible calcinosis from inflammation or traumatic injury. However,
histopathological and immunohistochemistry studies showed findings consistent with
a diagnosis of ES. She was treated with amputation of the interphalangeal joint of
the left thumb. This case highlights the clinical and pathologic correlation required
for the appropriate diagnosis and treatment of patients with soft tissue masses.
Key words
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Article info
Publication history
Published online: July 07, 2021
Accepted:
May 12,
2021
Received:
July 8,
2020
Footnotes
No benefits in any form have been received or will be received related directly or indirectly to the subject of this article.
Identification
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© 2022 by the American Society for Surgery of the Hand. All rights reserved.
