Purpose
To investigate the epidemiology of congenital upper limb anomalies (CULA) based on
the newly proposed Oberg, Manske, and Tonkin (OMT) classification, to compare this
classification with the International Federation of Societies for Surgery of the Hand
(IFSSH) classification, and to provide incidence rates of the different CULA.
Methods
In this study, the same 562 individuals with a CULA who were analyzed in a previous
epidemiologic study based on the IFSSH classification were reclassified according
to the OMT classification. All children identified with CULA and born in Stockholm
County between January 1, 1997 and December 31, 2007 were included in the study. During
the period there were 261,914 live births in Stockholm County, and the population
of Stockholm County was 1,949,516 inhabitants at the end of the period. From medical
records and available radiographs, all cases were analyzed regarding type of CULA,
sex, affected side, associated nonhand anomalies, and occurrence among relatives.
Individuals with right and left side anomalies belonging to different OMT subgroups
were counted as 2 anomalies; thus, the material consisted of 577 CULA in 562 children.
Results
It was possible to organize all CULA into the OMT classification. The largest main
category was malformations (429 cases), followed by deformations (124 cases), dysplasias
(10 cases), and syndromes (14 cases). We present the relation between the IFSSH and
OMT classifications, elucidate difficulties within the OMT classification, and propose
additions to the classification.
Conclusions
This study confirms that the OMT classification is useful and accurate, but also points
out difficulties. With further refinements, we regard the OMT classification as a
needed and appropriate replacement for the IFSSH classification.
Type of study/level of evidence
Diagnostic III.
Key words
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Article info
Publication history
Accepted:
November 4,
2013
Received:
August 6,
2013
Footnotes
Supported by grants from the Karolinska Institutet.
No benefits in any form have been received or will be received related directly or indirectly to the subject of this article.
Identification
Copyright
© 2014 American Society for Surgery of the Hand. Published by Elsevier Inc. All rights reserved.
